Read more about this disease, some with Classification – Types – Signs and symptoms – Genetics – Pathophysiology – Diagnosis – Screening – Prevention – Treatment and management – Cures and much more, some including pictures and video when available.
Mondini Dysplasia, (Mondini malformation, Mondini defect) is an abnormality in the inner ear that can be the cause of hearing loss.
A person with Mondini dysplasia has a cochlea that is incomplete. A normal cochlea has two and a half turns, a cochlea with Mondina dysplasia has two, one and a half, one, or no turns (or increments, obviously). This results in gradual or even sudden hearing loss that may be profound.”case history”. http://www.jpgmonline.com/article.asp?issn=0022-3859;year=2001;volume=47;issue=4;spage=272;epage=3;aulast=Shah.
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