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Dermatopathia pigmentosa reticularis (DPR) is a rare, autosomal dominant[1] congenital disorder that is a form of ectodermal dysplasia. Dermatopathia pigmentosa reticularis is composed of the triad of generalized reticulate hyperpigmentation, noncicatricial alopecia, and onychodystrophy.[2]:856
Symptoms include lack of sweat glands, thin hair, brittle nails, mottled skin, and lack of fingerprints.
DPR is comparable to Naegeli syndrome, both of which are caused by a specific defect in the keratin 14 protein.[3]
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